This website is for qualified health professionals. Please ensure you have read the Website Terms of Use.

Complications in Cystic Fibrosis

cfphysio.com

Complications in Cystic Fibrosis

LESSON 1: HAEMOPTYSIS

Button BM, Wilson C, Dentice R, Cox N, Middleton A, Tannenbaum E, Bishop J, Cobb R, Burton K, Wood M, Moran F, Black R, Bowen S, Day R, Depiazzi J, Doiron K, Doumit M, Dwyer T, Elliot A, Fuller L, Hall K, Hutchins M, Kerr M, Lee A, Mans C, O’Connor L, Steward R, Potter A, Rasekaba T, Scoones R, Tarrant B, Ward N, West S, White D, Wilson L, Wood J, Holland AE. Physiotherapy for Cystic Fibrosis in Australia and New Zealand: A Clinical Practice Guideline. Respirology2016; 21: 656–667

Flume PA, Mogayzel PJ, Robinson KA, et al. Cystic Fibrosis Pulmonary Guidelines: Pulmonary Complications: Hemoptysis and Pneumothorax. Am J Respir Crit Care Med. 2010 Aug 1;182(3):298-306. Paediatric Respiratory Reviews 2012 (13) 200 – 205.

Standards of Care and Good Clinical Practice for the Physiotherapy Management of Cystic Fibrosis. Third Edition April 2017 https://www.cysticfibrosis.org.uk/

https://www.cff.org/CF-Community-Blog/Posts/2017/Setting-the-Record-Straight-About-Coughing-Up-Blood/

http://www.torontoadultcf.com/cf-information/hemoptysis-0

LESSON 2: PNEUMOTHORAX

Button BM, Wilson C, Dentice R, Cox N, Middleton A, Tannenbaum E, Bishop J, Cobb R, Burton K, Wood M, Moran F, Black R, Bowen S, Day R, Depiazzi J, Doiron K, Doumit M, Dwyer T, Elliot A, Fuller L, Hall K, Hutchins M, Kerr M, Lee A, Mans C, O’Connor L, Steward R, Potter A, Rasekaba T, Scoones R, Tarrant B, Ward N, West S, White D, Wilson L, Wood J, Holland AE. Physiotherapy for Cystic Fibrosis in Australia and New Zealand: A Clinical Practice Guideline. Respirology2016; 21: 656–667

Flume PA, Mogayzel PJ, Robinson KA, et al. Cystic Fibrosis Pulmonary Guidelines: Pulmonary Complications: Hemoptysis and Pneumothorax. Am J Respir Crit Care Med. 2010 Aug 1;182(3):298-306. Paediatric Respiratory Reviews 2012 (13) 200 – 205.

Standards of Care and Good Clinical Practice for the Physiotherapy Management of Cystic Fibrosis. Third Edition April 2017 https://www.cysticfibrosis.org.uk/

LESSON 3: URINARY STRESS INCONTINENCE

Button BM, Wilson C, Dentice R, Cox N, Middleton A, Tannenbaum E, Bishop J, Cobb R, Burton K, Wood M, Moran F, Black R, Bowen S, Day R, Depiazzi J, Doiron K, Doumit M, Dwyer T, Elliot A, Fuller L, Hall K, Hutchins M, Kerr M, Lee A, Mans C, O’Connor L, Steward R, Potter A, Rasekaba T, Scoones R, Tarrant B, Ward N, West S, White D, Wilson L, Wood J, Holland AE. Physiotherapy for Cystic Fibrosis in Australia and New Zealand: A Clinical Practice Guideline. Respirology2016; 21: 656–667

McVean R, Orr A, Webb AK, Bradbury A, Kay L, Phillips E, Dodd ME. Treatment of urinary incontinence in cystic fibrosis. Journal of Cystic Fibrosis 2003;4: 171-176

Standards of Care and Good Clinical Practice for the Physiotherapy Management of Cystic Fibrosis. Third Edition April 2017 https://www.cysticfibrosis.org.uk/

Lesson Four: Liver disease in CF

Colombo C, Crosignani A, Battezzati PM. Liver involvement in cystic fibrosis. J Hepatol 1999; 31: 946-954

Desai CS et al. Survival of cystic fibrosis patients undergoing liver and liver-lung transplantations. Transplantation proceedings. 2013; vol.45, no.1, p.290-292.

Moyer K, Balistreri W. Hepatobiliary disease in patients with cystic fibrosis. Curr Opin Gastroenterol. 2009;25(3):272-8.

Parisi GF et al. Liver disease in cystic fibrosis: an update. Hepatitis monthly. 2013; 13; 8, p 1735-1743

LESSON 5: PREGNANCY IN CF

Ahluwalia M, Hong J, Hadeh A, Ferrin M, Hadjiliadis D. Cystic Fibrosis and pregnancy in the modern era: A case control study. Journal of Cystic Fibrosis. 2014. 13.69-73

Button, B. M., Wilson, C., Dentice, R., Cox, N. S., Middleton, A., Tannenbaum, E., Bishop, J., Cobb, R., Burton, K., Wood, M., Moran, F., Black, R., Bowen, S., Day, R., Depiazzi, J., Doiron, K., Doumit, M., Dwyer, T., Elliot, A., Fuller, L., Hall, K., Hutchins, M., Kerr, M., Lee, A. L., Mans, C., O’Connor, L.,Steward, R., Potter, A., Rasekaba, T., Scoones, R., Tarrant, B., Ward, N., West, S., White, D.,Wilson, L., Wood, J., and Holland, A. E. (2016) Physiotherapy for cystic fibrosis in Australia and New Zealand: A clinical practice guideline. Respirology, 21: 656–667.

Edenborough F, Borgo G, Knoop C, Lannerfors L, Mackenzie W, Madge S, Morton A, Oxley H, Touw D, Benham M, Johannesson M. Guidelines for management of pregnancy in women with cystic Fibrosis. Journal of Cystic Fibrosis. 2008. 7: S2-S32.

Grigoriadis C, Tympa A, Theodoraki K. Cystic Fibrosis and preganancy counselling, obstetrical management and prenatal outcomes. Invest Clin. 2015. 56(1). 66-73

Johannesson M. Effects of pregnancy on health: certain aspects of importance for women with CF. Journal of Cystic Fibrosis. 2002. 1: 9-12.

LESSON 6: CYSTIC FIBROSIS RELATED DIABETES

Brunzell C, hardin D, Kogler A, Moran A, Schindler T. Managing CFRD.Cystic Fibrosis Foundation Guidelines.2015.

Button, B. M., Wilson, C., Dentice, R., Cox, N. S., Middleton, A., Tannenbaum, E., Bishop, J., Cobb, R., Burton, K., Wood, M., Moran, F., Black, R., Bowen, S., Day, R., Depiazzi, J., Doiron, K., Doumit, M., Dwyer, T., Elliot, A., Fuller, L., Hall, K., Hutchins, M., Kerr, M., Lee, A. L., Mans, C., O’Connor, L.,Steward, R., Potter, A., Rasekaba, T., Scoones, R., Tarrant, B., Ward, N., West, S., White, D.,Wilson, L., Wood, J., and Holland, A. E. (2016) Physiotherapy for cystic fibrosis in Australia and New Zealand: A clinical practice guideline. Respirology, 21: 656–667.

Middleton P, Wagenaar M, Matson A, Craig M, Holmes-Walker D, Katz T, Hameed S. Australian standards of care for CFRD. Respirology. 2014. 19: 185-192.

Moran A, Brunzell C, Cohen RC, Katz M, Marshall BC, Onady G, Robinson KA, Sabadosa KA, Stecenko A, Slovis B. Clinical care guidelines for cystic fibrosis-related diabetes: a position statement of the American Diabetes Association and a clinical practice guideline of the Cystic Fibrosis Foundation, endorsed by the Pediatric Endocrine Society. Diabetes Care. 2010; 33: 2697-708

https://www.cff.org/Life-With-CF/Daily-Life/Cystic-Fibrosis-related-Diabetes/Managing-CFRD.pdf

LESSON 7: CYSTIC FIBROSIS BONE DISEASE

Buntain HM, Greer RM, Schluter PJ, Wong JC, Batch JA, Potter JM, Lewindon PJ, Powell E, Wainwright CE, Bell SC. Bone mineral density in Australian children, adolescents and adults with cystic fibrosis: a controlled cross sectional study. Thorax. 2004; 59: 149-55.

Button, B. M., Wilson, C., Dentice, R., Cox, N. S., Middleton, A., Tannenbaum, E., Bishop, J., Cobb, R., Burton, K., Wood, M., Moran, F., Black, R., Bowen, S., Day, R., Depiazzi, J., Doiron, K., Doumit, M., Dwyer, T., Elliot, A., Fuller, L., Hall, K., Hutchins, M., Kerr, M., Lee, A. L., Mans, C., O’Connor, L.,Steward, R., Potter, A., Rasekaba, T., Scoones, R., Tarrant, B., Ward, N., West, S., White, D.,Wilson, L., Wood, J., and Holland, A. E. (2016) Physiotherapy for cystic fibrosis in Australia and New Zealand: A clinical practice guideline. Respirology, 21: 656–667

Grey V, Atkinson S, Drury D, Casey L, Ferland G, Gundberg C, Lands LC. Prevalence of low bone mass and deficiencies of vitamins D and K in pediatric patients with cystic fibrosis from 3 Canadian centers. Pediatrics. 2008; 122: 1014-20

Haworth CS. Impact of cystic fibrosis on bone health. Current opinion in pulmonary medicine. 2010; 16: 616-22

Hind K, Truscott JG, Conway SP. Exercise during childhood and adolescence: a prophylaxis against cystic fibrosis-related low bone mineral density? Exercise for bone health in children with cystic fibrosis. Journal of Cystic Fibrosis. 2008; 7: 270-6

Tejero Garcia S, Giraldez Sanchez MA, Cejudo P, Quintana Gallego E, Dapena J, Garcia Jimenez R, Cano Luis P, Gomez de Terreros I. Bone health, daily physical activity, and exercise tolerance in patients with cystic fibrosis. Chest. 2011; 140: 475-81

slider3

Website Terms of Use

All content and media on the CFPhysio website is created and published online for information purposes only. Before viewing the content on the this website you should read the website terms of use and privacy policy. The content in this website is not intended to be a substitute for professional medical advice and should not be relied upon as medical advice. If you have any concerns about your health, or concerns are raised from information on this website, please contact your treating doctor, qualified health professional or local clinic.